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P504S rabbit pAb
商品貨號： PLA021347
適 應(yīng) 性： 人,小鼠,大鼠
WB ELISA
￥600元
規(guī)格：
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MSDS
說明書
商品描述
  • 基因名稱： AMACR
  • 蛋白名稱： P504S
  • Human_gene_id： 23600
  • Human_gene_link： http://www.ncbi.nlm.nih.gov/sites/entrez?db=gene&term=23600
  • Human_swiss_prot_no： Q9UHK6
  • Human_swiss_link： https://www.uniprot.org/uniprotkb/Q9UHK6/entry
  • Mouse_gene_id： 17117
  • Mouse_gene_link： https://www.uniprot.org/uniprot/17117
  • Mouse_swiss_prot_no： O09174
  • Mouse_swiss_link： https://www.uniprot.org/uniprotkb/O09174
  • Rat_swiss_prot_no： P70473
  • Rat_swiss_link： https://www.uniprot.org/uniprotkb/P70473
  • 特異性： This antibody detects endogenous levels of Human,Mouse,Rat P504S
  • 組成： Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide.
  • 來源： Polyclonal, Rabbit,IgG
  • 稀釋： WB 1:1000-2000 ELISA 1:5000-20000
  • 純化工藝： The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.
  • 濃度： 1 mg/ml
  • 儲存： -15°C to -25°C/1 year(Do not lower than -25°C)
  • 說明書： 1
  • Msds： MSDS_Antibody.pdf
  • 其他名稱： Alpha-methylacyl-CoA racemase (EC 5.1.99.4;2-methylacyl-CoA racemase)
  • 分子量： 42kD
  • 功能： catalytic activity:(2S)-2-methylacyl-CoA = (2R)-2-methylacyl-CoA.,disease:Defects in AMACR are the cause of alpha-methylacyl-CoA racemase deficiency (AMACRD) [MIM:604489]. AMACRD results in elevated plasma concentrations of pristanic acid C27-bile-acid intermediates. It can be associated with polyneuropathy, retinitis pigmentosa, epilepsy.,disease:Defects in AMACR are the cause of congenital bile acid synthesis defect type 4 (CBAS4) [MIM:214950]; also known as cholestasis, intrahepatic, with defective conversion of trihydroxycoprostanic acid to cholic acid or trihydroxycoprostanic acid in bile. Clinical features include neonatal jaundice, intrahepatic cholestasis, bile duct deficiency and absence of cholic acid from bile.,function:Racemization of 2-methyl-branched fatty acid CoA esters. Responsible for the conversion of pristanoyl-CoA and C27-bile acyl-CoAs to their (S)-stereoisomers.,pathway:Lipid metabolism; bile acid biosynthesis.,pathway:Lipid metabolism; fatty acid metabolism.,similarity:Belongs to the caiB/baiF CoA-transferase family.,similarity:Contains 1 C1q domain.,similarity:Contains 1 collagen-like domain.,
  • 相關(guān)產(chǎn)品： RS0001,RS0002,YM3028,YM3364
  • 細(xì)胞定位： Peroxisome . Mitochondrion .
  • 科研貨號： PLA021347
P504S rabbit pAb
Catalog No PLA021347
Product information
  • 基因名稱： AMACR
  • 蛋白名稱： P504S
  • Human_gene_id： 23600
  • Human_gene_link： http://www.ncbi.nlm.nih.gov/sites/entrez?db=gene&term=23600
  • Human_swiss_prot_no： Q9UHK6
  • Human_swiss_link： https://www.uniprot.org/uniprotkb/Q9UHK6/entry
  • Mouse_gene_id： 17117
  • Mouse_gene_link： https://www.uniprot.org/uniprot/17117
  • Mouse_swiss_prot_no： O09174
  • Mouse_swiss_link： https://www.uniprot.org/uniprotkb/O09174
  • Rat_swiss_prot_no： P70473
  • Rat_swiss_link： https://www.uniprot.org/uniprotkb/P70473
  • 特異性： This antibody detects endogenous levels of Human,Mouse,Rat P504S
  • 組成： Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide.
  • 來源： Polyclonal, Rabbit,IgG
  • 稀釋： WB 1:1000-2000 ELISA 1:5000-20000
  • 純化工藝： The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.
  • 濃度： 1 mg/ml
  • 儲存： -15°C to -25°C/1 year(Do not lower than -25°C)
  • 說明書： 1
  • Msds： MSDS_Antibody.pdf
  • 其他名稱： Alpha-methylacyl-CoA racemase (EC 5.1.99.4;2-methylacyl-CoA racemase)
  • 分子量： 42kD
  • 功能： catalytic activity:(2S)-2-methylacyl-CoA = (2R)-2-methylacyl-CoA.,disease:Defects in AMACR are the cause of alpha-methylacyl-CoA racemase deficiency (AMACRD) [MIM:604489]. AMACRD results in elevated plasma concentrations of pristanic acid C27-bile-acid intermediates. It can be associated with polyneuropathy, retinitis pigmentosa, epilepsy.,disease:Defects in AMACR are the cause of congenital bile acid synthesis defect type 4 (CBAS4) [MIM:214950]; also known as cholestasis, intrahepatic, with defective conversion of trihydroxycoprostanic acid to cholic acid or trihydroxycoprostanic acid in bile. Clinical features include neonatal jaundice, intrahepatic cholestasis, bile duct deficiency and absence of cholic acid from bile.,function:Racemization of 2-methyl-branched fatty acid CoA esters. Responsible for the conversion of pristanoyl-CoA and C27-bile acyl-CoAs to their (S)-stereoisomers.,pathway:Lipid metabolism; bile acid biosynthesis.,pathway:Lipid metabolism; fatty acid metabolism.,similarity:Belongs to the caiB/baiF CoA-transferase family.,similarity:Contains 1 C1q domain.,similarity:Contains 1 collagen-like domain.,
  • 相關(guān)產(chǎn)品： RS0001,RS0002,YM3028,YM3364
  • 細(xì)胞定位： Peroxisome . Mitochondrion .
  • 科研貨號： PLA021347
    • Hunan UPT Biotechnology Co.,Ltd
    Website：www.hnntwy.com Servive hotline :4006916686
    E-mail：service@uptbio.com
    Address：
    Room 402, Building 13, Xinggong International Industrial Park, 100 Guyuan Road, Yuelu District, Changsha City, Hunan Province, China.
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