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DYM rabbit pAb
商品貨號(hào)： PLA020756
適 應(yīng) 性： 人,小鼠,大鼠
WB
￥600元
規(guī)格：
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MSDS
說明書
商品描述
  • 基因名稱： DYM
  • 蛋白名稱： DYM
  • Human_gene_id： 54808
  • Human_gene_link： http://www.ncbi.nlm.nih.gov/sites/entrez?db=gene&term=54808
  • Human_swiss_prot_no： Q7RTS9
  • Human_swiss_link： https://www.uniprot.org/uniprotkb/Q7RTS9/entry
  • Mouse_gene_id： 69190
  • Mouse_gene_link： https://www.uniprot.org/uniprot/69190
  • Mouse_swiss_prot_no： Q8CHY3
  • Mouse_swiss_link： https://www.uniprot.org/uniprotkb/Q8CHY3
  • Rat_swiss_prot_no： B4F766
  • Rat_swiss_link： https://www.uniprot.org/uniprotkb/B4F766
  • 特異性： This antibody detects endogenous levels of DYM at Human/Mouse/Rat
  • 組成： Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide.
  • 來源： Polyclonal, Rabbit,IgG
  • 稀釋： WB 1：500-2000
  • 純化工藝： The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.
  • 濃度： 1 mg/ml
  • 儲(chǔ)存： -15°C to -25°C/1 year(Do not lower than -25°C)
  • 說明書： 1
  • Msds： MSDS_Antibody.pdf
  • 分子量： 74kD
  • 功能： disease:Defects in DYM are the cause of Dyggve-Melchior-Clausen syndrome (DMC) [MIM:223800]. DMC is a rare autosomal recessive disorder characterized by short trunk dwarfism, microcephaly and psychomotor retardation. Electron microscopic study of cutaneous cells of affected patients shows dilated rough endoplasmic reticulum, enlarged and aberrant vacuoles and numerous vesicles. DMC is progressive.,disease:Defects in DYM are the cause of Smith-McCort dysplasia (SMC) [MIM:607326]. SMC is a rare autosomal recessive osteochondrodysplasia characterized by short limbs and trunk with barrel-shaped chest. The radiographic phenotype includes platyspondyly, generalized abnormalities of the epiphyses and metaphyses, and a distinctive lacy appearance of the iliac crest, features identical to those of Dyggve-Melchior-Clausen syndrome.,PTM:Myristoylated in vitro; myristoylation is not essential for protein targeting to Golgi compartment.,similarity:Belongs to the dymeclin family.,subcellular location:Sequence analysis programs clearly predict 1 transmembrane region. However, PubMed:18996921 shows that it is not a stably anchored transmembrane protein but it weakly associates with the Golgi apparatus and shuttles between the Golgi and the cytosol.,tissue specificity:Expressed in most embryo-fetal and adult tissues. Abundant in primary chondrocytes, osteoblasts, cerebellum, kidney, lung, stomach, heart, pancreas and fetal brain. Very low or no expression in the spleen, thymus, esophagus, bladder and thyroid gland.,
  • 相關(guān)產(chǎn)品： RS0001,RS0002,YM3028,YM3029
  • 細(xì)胞定位： Cytoplasm. Golgi apparatus. Membrane ; Lipid-anchor . Sequence analysis programs clearly predict 1 transmembrane region. However, PubMed:18996921 shows that it is not a stably anchored transmembrane protein but it weakly associates with the Golgi apparatus and shuttles between the Golgi and the cytosol.
  • 組織表達(dá)： Expressed in most embryo-fetal and adult tissues. Abundant in primary chondrocytes, osteoblasts, cerebellum, kidney, lung, stomach, heart, pancreas and fetal brain. Very low or no expression in the spleen, thymus, esophagus, bladder and thyroid gland.
  • 科研貨號(hào)： PLA020756
DYM rabbit pAb
Catalog No PLA020756
Product information
  • 基因名稱： DYM
  • 蛋白名稱： DYM
  • Human_gene_id： 54808
  • Human_gene_link： http://www.ncbi.nlm.nih.gov/sites/entrez?db=gene&term=54808
  • Human_swiss_prot_no： Q7RTS9
  • Human_swiss_link： https://www.uniprot.org/uniprotkb/Q7RTS9/entry
  • Mouse_gene_id： 69190
  • Mouse_gene_link： https://www.uniprot.org/uniprot/69190
  • Mouse_swiss_prot_no： Q8CHY3
  • Mouse_swiss_link： https://www.uniprot.org/uniprotkb/Q8CHY3
  • Rat_swiss_prot_no： B4F766
  • Rat_swiss_link： https://www.uniprot.org/uniprotkb/B4F766
  • 特異性： This antibody detects endogenous levels of DYM at Human/Mouse/Rat
  • 組成： Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide.
  • 來源： Polyclonal, Rabbit,IgG
  • 稀釋： WB 1：500-2000
  • 純化工藝： The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.
  • 濃度： 1 mg/ml
  • 儲(chǔ)存： -15°C to -25°C/1 year(Do not lower than -25°C)
  • 說明書： 1
  • Msds： MSDS_Antibody.pdf
  • 分子量： 74kD
  • 功能： disease:Defects in DYM are the cause of Dyggve-Melchior-Clausen syndrome (DMC) [MIM:223800]. DMC is a rare autosomal recessive disorder characterized by short trunk dwarfism, microcephaly and psychomotor retardation. Electron microscopic study of cutaneous cells of affected patients shows dilated rough endoplasmic reticulum, enlarged and aberrant vacuoles and numerous vesicles. DMC is progressive.,disease:Defects in DYM are the cause of Smith-McCort dysplasia (SMC) [MIM:607326]. SMC is a rare autosomal recessive osteochondrodysplasia characterized by short limbs and trunk with barrel-shaped chest. The radiographic phenotype includes platyspondyly, generalized abnormalities of the epiphyses and metaphyses, and a distinctive lacy appearance of the iliac crest, features identical to those of Dyggve-Melchior-Clausen syndrome.,PTM:Myristoylated in vitro; myristoylation is not essential for protein targeting to Golgi compartment.,similarity:Belongs to the dymeclin family.,subcellular location:Sequence analysis programs clearly predict 1 transmembrane region. However, PubMed:18996921 shows that it is not a stably anchored transmembrane protein but it weakly associates with the Golgi apparatus and shuttles between the Golgi and the cytosol.,tissue specificity:Expressed in most embryo-fetal and adult tissues. Abundant in primary chondrocytes, osteoblasts, cerebellum, kidney, lung, stomach, heart, pancreas and fetal brain. Very low or no expression in the spleen, thymus, esophagus, bladder and thyroid gland.,
  • 相關(guān)產(chǎn)品： RS0001,RS0002,YM3028,YM3029
  • 細(xì)胞定位： Cytoplasm. Golgi apparatus. Membrane ; Lipid-anchor . Sequence analysis programs clearly predict 1 transmembrane region. However, PubMed:18996921 shows that it is not a stably anchored transmembrane protein but it weakly associates with the Golgi apparatus and shuttles between the Golgi and the cytosol.
  • 組織表達(dá)： Expressed in most embryo-fetal and adult tissues. Abundant in primary chondrocytes, osteoblasts, cerebellum, kidney, lung, stomach, heart, pancreas and fetal brain. Very low or no expression in the spleen, thymus, esophagus, bladder and thyroid gland.
  • 科研貨號(hào)： PLA020756
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